Intracranial Septum Pellucidum Dysembryoplastic Neuroepithelial Tumor: Case Presentation and Review of Pediatric Septum Pellucidum Tumors

Rimal Dossani, MD, Devi Patra, MD, Nimer Adeeb, MD, Elizabeth Wild, MD, Abhilasha Ghildyal, MD, Marjorie Fowler, MD, Christina Notarianni, MD


Dysembryoplastic neuroepithelial tumors (DNETs) of the septum pellucidum are a rare location for DNETs, which are most commonly located in the temporal cortex. In this case report, we present the case of a 5-year-old boy who presented with seizures. Magnetic resonance imaging (MRI) revealed a hyperintense mass on T2-weighted imaging arising from the right septum pellucidum. The patient was placed in right lateral decubitus position and underwent right interhemispheric craniotomy for resection of mass. Gross total resection was achieved and pathology was consistent with DNET. Patient has been free of seizures since the time of operation and MRI scans have been free of recurrence. We review the molecular and histopathological features of DNETs. Most importantly, for the interest of the general medical community, we present a differential diagnosis of pediatric septum pellucidum tumors based on MRI and histopathological findings.

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